Segmental Neurofibromatosis with Angiolipomas

Abstract

A 28 year old male had right axillary freckling, a few cafe-aulait macules and numerous freckles over the right upper half of his body involving the -scapular region, shoulder, chest wall, upper arm and proximal half of the forearm Numerous, bilateral subcutaneous nodules which could possibly be dismissed clinically as subcutaneous nodules of neurofibromatosis, proved to be angiolipomas histopathologically. It is suggested that in the cal molluscum fibrosum, histopathology of subcutaneous nodules should always be resorted to in suspected cases of Neurofibromatosis even when there are suggestive pigmentary changes.