Cowden syndrome – Report of two cases
T V Gopalakrishnan Nair
Department of Dermatology and Venereology, Medical college Hospital, Trivandrum - 695011
|How to cite this article:
Usha V, Gopalakrishnan Nair T V, Yogirajan K. Cowden syndrome – Report of two cases. Indian J Dermatol Venereol Leprol 1999;65:42-43
Two case of Cowden syndrome with typical features are presented. In addition to the cutaneous lesions like facial trichilemmomas, oral mucosal fibromas, acrokeratosis verruciformis and palmo plantar hyperkeratosis, the first patient had follicular carcinoma of thyroid, fibrocystic disease of the breasts and ovarian teratoma and second patient had a cerebellar hamartoma (Lhermitte Duelos syndrome) which is a rare entity.